成人泌尿系横纹肌肉瘤的诊治及预后(附8例报告及文献复习)

王雪刚; 章小平; 陈力; 王荣; 陈宣余; 韩伟伟; 曾甫清; 肖亚军; 赵军; 庞自力; 陈敏; 范民

成人泌尿系横纹肌肉瘤的诊治及预后(附8例报告及文献复习)

- 华中科技大学同济医学院附属协和医院泌尿外科(武汉, 430022)

详细信息

通讯作者: 章小平,E-mail:xiaoping.zhang2008@gmail.com

中图分类号: R737

收稿日期: 2012-12-04

Diagnosis, treatment and prognosis of adult urinary rhabdomyosarcoma (Report of 8 cases and review of literature)

- Department of Urology, Union Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan, 430022, China

More Information

Corresponding author: ZHANG Xiaoping, E-mail: xiaoping.zhang2008@gmail.com

Received Date: 04 December 2012

摘要

摘要: 目的：探讨成人泌尿系横纹肌肉瘤的病变特点及临床诊治方法。方法：回顾性分析8例成人泌尿系横纹肌肉瘤患者的临床资料：男6例，女2例，发病年龄18~47岁，平均29.1岁。肿瘤位于膀胱3例，前列腺2例，睾丸旁2例，肾脏1例。结果：本组8例均确诊为横纹肌肉瘤，其中6例行手术治疗，术后给予化疗或放疗，另2例单纯给予化疗。2例1年内死亡，2例2年内死亡，4例仍在随访中。结论：成人泌尿系横纹肌肉瘤属少见病，恶性程度高，进展快，大多数患者就诊时已属晚期，治疗效果差，早发现、早诊断、早治疗及以手术为主的综合治疗方式能取得较好效果。
- 泌尿系肿瘤 /
- 横纹肌肉瘤 /
- 成人
Abstract: Objective: To explore the characteristics, clinical diagnosis and treatment of adult urinary rhabdomyosarcoma.Method: A retrospective chart review was carried out for 8 adult patients diagnosed with urinary rhabdomyosarcoma:Six cases were male, two cases were femcle. The average age was 29.1(range from 18-47). Rhabdomy osarcoma was loated in bladder(3 cases), prostare(2 cases), testis(2 cases), kidney(1 cases) respectively.Result: The eight cases were confirmed for rhabdomyosarcoma, including 6 patients underwent surgery and had postoperative chemotherapy and/or radiotherapy, the other two patients only treated with chemotherapy. 2 cases died within 1 year, 2 cases died within 2 years, 4 patients still under follow-up.Conclusion: Adult urinary rhabdomyosarcoma is a rare disease with high malignancy. Because their early symptoms are not typical and progress fast, most diagnosed patients were at the advanced stage and had poor prognosis. Being early detection and early diagnosis, surgical resection with chemotherapy and/or radiotherapy was an effective way to achieve favorable outcomes.
- urinary tumor /
- rhabdomyosarcoma /
- adult

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参考文献(9)

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