Diagnosis and management of primary epididymal sarcoma: a case report and literature review
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摘要: 目的：报告罕见原发性附睾肉瘤1例，并讨论其临床特点及诊疗原则。方法：首次报告附睾肌源性间叶源性肉瘤1例，并检索复习文献。结果：患者22岁，自觉左侧睾丸增大1月余， B超提示左侧附睾尾5.5 cm×4.2 cm混合回声占位，择期行左侧附睾肿物切除术，术后病理报告示附睾低分化肌源性间叶源性肉瘤。随即行患侧睾丸高位切除术。术后2个月发现腹膜后多发淋巴结转移，术后6个月发现双肺转移。附睾肉瘤国内外文献共报道37例。结论：附睾肉瘤极为罕见，中老年常见，恶性程度较高，治疗以睾丸高位切除为主，预后较差。Abstract: Objective: To discuss the clinical manifestation and treatment principle of primary epididymal sarcoma.Method: We firstly report a case of primary epididymal mesenchymal myogenic sarcoma, and review the literature.Result: A 22-year-old man complained left testis enlargement for 1 month, ultrasound showed a mass located in tail of epididymis (5.5 cm×4.2 cm). A transscrotal resection of the left epididymal lesion was performed later and pathologic examination revealed epidiymal mesenchymal myogenic sarcoma. A radical orchiectomy was preformed immediately. Retroperitoneal lymph node metastases were found 2 month later, and bilateral lung metastases was found in 6-month post-operation examination. Only 37 cases have been reported in world literature.Conclusion: The primary epididymal sarcoma is extremely rare with higher malignant degree and poor prognosis. The mainly treatment was radical orchiectomy.
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Key words:
- epididymal tumor /
- sarcoma /
- mesenchymal myogenic sarcoma /
- treatment
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