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摘要: 膀胱副神经节瘤是一种罕见的肿瘤疾病,因多位于黏膜下层和肌层之间,且具有潜在恶性,故极易误诊为膀胱尿路上皮癌。本例报道1例27岁女性膀胱副神经节瘤患者。该患者因“大量血尿”入院,彩超、CT、MRI均提示膀胱占位。全身麻醉下行经尿道膀胱肿瘤电切手术,术后组织病理及免疫组织化学提示副神经节瘤。出院后2周再次发生无痛性肉眼血尿,全身麻醉下行膀胱部分切除术,术后痊愈出院。正确地诊断膀胱副神经节瘤具有重要的临床价值,尤其是影像学检查对诊断至关重要。手术是膀胱副神经节瘤最有效的治疗方法,而膀胱部分切除术是膀胱副神经节瘤的主要手术方式。Abstract: Paraganglioma of urinary bladder (PUB) is a rare tumor. As PUB mostly lies between submucosa and muscularis and has potential malignancy, it is very easy to be misdiagnosed as bladder urothelial carcinoma. This is the case report of a twenty-seven female patient with PUB. The patient was admitted due to 'massive hematuria'. Ultrasound, CT and MRI all showed space occupying lesion of bladder. The patient underwent transurethral resection of bladder tumor (TURBT). Paraganglioma was revealed by histopathology and immunohistochemistry. Painless hematuria occurred again 2 weeks after leaving hospital. Hence, the patient underwent partial cystectomy (PC) and be cured. It is important to diagnosis of PUB correctly, in particular for radiology. Surgery is the most effective treatment for PUB, and PC is the dominant surgical method for PUB.
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Key words:
- paraganglioma /
- urinary bladder /
- partial cystectomy
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