局限性膀胱淀粉样变1例报告并文献复习

辛海贝; 严景民; 周高标; 穆大为; 郑杰; 蔡月宁; 魏小龙; 郭和清

局限性膀胱淀粉样变1例报告并文献复习

- 1. 安徽医科大学空军临床学院(北京, 100142);
- 2. 解放军空军总医院泌尿外科

详细信息

通讯作者: 郭和清,E-mail:guoheqing@sina.com.cn

中图分类号: R694

收稿日期: 2012-01-03

Localized amyloidosis of the urinary bladder: A case report and review of literature

- (1. Air Force Clinical College, Anhui Medical University, Beijing, 100142, China;
- 2. Department of Urology, Air Force General Hospital of PLA

More Information

Corresponding author: GUO Heqing, E-mail: guoheqing@sina.com.cn

Received Date: 03 January 2012

摘要

摘要: 目的：探讨局限性膀胱淀粉样变病因、临床表现、影像学诊断方法、病理特征及诊疗方法。方法：回顾分析1例局限性膀胱淀粉样变患者的临床资料，总结复习相关文献。结果：患者经抗感染、止血、对症治疗，效果较好，随访7个月未复发血尿。结论：膀胱淀粉样变为少见病，主要表现为无痛性肉眼血尿，膀胱侧壁和三角区为好发部位，确诊主要依靠膀胱镜下活检，病理学检查刚果红染色后偏振光显微镜下呈现出苹果绿色双折射光。治疗以手术切除为主，术后辅以二甲基亚砜膀胱灌注，疗效及预后良好。
- 膀胱淀粉样变 /
- 刚果红染色 /
- 诊治 /
- 预后
Abstract: Objective: To detect the etiopathogenisis, clinical, radiological, pathological characteristics, diagnostic and therapic methods of localized amyloidosis of the urinary bladder. Method: The clinical and pathological data of one case of localized urinary bladder amyloidosis was retrospectively analysed. And we reviewed and summarized literatures.Result: The patient recovered though the treatment of anti-inflammatory hemostasis and symptomatic treatment, and hematuria did not recur within 7 months. Conclusion: Localized amyloidosis of the urinary bladder is a rare disease which manifested painless gross hematuria usually. The lateral wall and trigone of the bladder are commonly affected areas. Definitive diagnosis rested on examination of a biopsy specimen and Congo red dye. The prognosis is good after the treatments of trans-urethral resection and supplemented with intravesical DMSO instillation.
- bladder amyloidosis /
- congo red staining /
- diagnosis, treatment /
- prognosis

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参考文献(16)

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